IgG4-related retroperitoneal fibrosis: a newly characterized disease
نویسندگان
چکیده
منابع مشابه
Pathologically Proven Spontaneous Remission of IgG4-related Retroperitoneal Fibrosis
Some forms of idiopathic retroperitoneal fibrosis (RF) have recently been considered to be a part of the spectrum of immunoglobulin G4 (IgG4)-related disease. This case report is the first description of a spontaneous remission in a patient with pathologically proven IgG4-related RF. Although the pathogenesis and long-term disease behavior of IgG4-related RF remains unknown, we believe that an ...
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Immunoglobulin G4-related disease (IgG4-RD) is a newly recognized fibroinflammatory condition which can potentially involve any organ. Some characteristic histopathologic features with lymphoplasmacytic infiltrate, an increased number of IgG4+ cells, storiform fibrosis and obliterative phlebitis are the mainstay for diagnosis. Serum IgG4 levels often increase. We report the case of a patient wi...
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ژورنال
عنوان ژورنال: International Journal of Rheumatic Diseases
سال: 2016
ISSN: 1756-1841
DOI: 10.1111/1756-185x.12863